Abstract
Primary retroperitoneal mucinous cystadenomas (PRMC) are rare benign neoplasms with only 55 documented cases in the English literature so far. A 19-year-old female exhibited hirsutism and was found to have a cystic mass measuring 5.8 cm × 3.9 cm × 5.8 cm in the left retroperitoneum. During subsequent workup a high pre-operative value of dehydroepiandrosterone sulfate (DHEAS) was noted. The patient was referred to surgical oncology and underwent an uneventful laparoscopic cystectomy. Pathology classified the cyst as PRMC. Post-operatively, the patient’s DHEAS levels normalized, though there was no appreciable decrease in the patient’s hirsutism in the short term follow-up. The origin of PRMC is uncertain. Due to their unknown biological potential, surgical resection is usually recommended. To the best of our knowledge, this is the first report documenting a PRMC and elevated levels of androgens in conjunction with hirsutism.
- benign retroperitoneal tumor
- mucinous cystadenoma
- primary retroperitoneal mucinous cystadenoma
- retroperitoneum
- hirsutism
- Received February 19, 2019.
- Revision received July 18, 2019.
- Accepted August 5, 2019.
